What Is Prune Belly Syndrome?
Source: Genetic and Rare Diseases (GARD) Information Center
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Prune Belly Syndrome
PBS; Eagle-Barrett Syndrome; Obrinsky Syndrome; Triad Syndrome
Prune belly syndrome, or PBS, is a group of birth defects characterized by a lack of abdominal muscles, causing the skin on the abdominal area to wrinkle and appear "prune-like"; undescended testicles in males; and urinary tract malformations. Explore symptoms, causes, and genetics.
Baby
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Prune belly syndrome - A. At birth B. At nine years of age (surgical scars noted from a prior abdominoplasty procedure)
Image by Senthilkumar Sankararaman, MD - Copyright © 2023, StatPearls Publishing LLC
Source: Genetic and Rare Diseases (GARD) Information Center
Unknown (película)
Image by Diseñadores publicitarios/Wikimedia
Source: Genetic and Rare Diseases (GARD) Information Center
Prune belly syndrome
Image by Kotb A Metwalley, Hekma S Farghalley and Alaa A Abd-Elsayed
Source: Genetic and Rare Diseases (GARD) Information Center
Surgery
Image by Staff Sgt. Miguel Lara/Wikimedia
Source: Genetic and Rare Diseases (GARD) Information Center
Treatment and Prognosis varies depending on the type of condition and the age of symptom onset.
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The prognosis associated with prune belly syndrome varies depending several factors including the severity of the underlying tract anomaly, how well the kidneys are developed, and the likelihood of renal failure. The condition can become life threatening in severely affected children; however, mild cases might be limited to undescended testicles and a small amount of abdominal wall laxity. Studies have found that 30% of individuals with prune belly syndrome require kidney transplantation in their lifetime.
Despite these concerns, many individuals with prune belly syndrome report having good physical and mental health as well as a good overall quality of life.
Source: Genetic and Rare Diseases (GARD) Information Center
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