Since EHE is so rare, there is no standard treatment. Treatment for each person is different and depends on where in the body EHE starts and if it has spread. You should see a doctor who is an expert in tumors that form in blood vessels to decide the best approach for your cancer. You can contact MyPART for help finding experts near you.
Surgery:
Surgery is most often used to treat EHE that has not spread to other parts of the body. Surgery can also be used with chemotherapy and radiation therapy.
Radiation therapy:
Doctors sometimes use radiation therapy to treat EHE, with or without surgery. Radiation therapy is most often used to treat EHE that grows in the bones. Because radiation therapy can cause other cancers in the future, it is important to discuss this option with your doctor.
Chemotherapy:
Doctors may use chemotherapy with other treatments. It is important to discuss the side effects with your doctor.
Targeted therapy:
Because EHE is made up of cells that form blood vessels, some doctors are trying treatments that target tumor blood vessels. These treatments are called anti-angiogenics.
Immunotherapy:
Immunotherapy uses different treatments to help the body’s immune system kill tumor cells.
Watch and wait:
In some cases, the tumor grows very slowly, or even shrinks without any treatment. In this case it may be safest for your doctor to check your tumor often without treating it.
Embolization:
In some cases, blocking the blood flow to the tumor, called embolization, can help shrink and kill the tumor.